Vasculitis & polymyalgia rheumatica

Pulmonary artery involvement due to Behçet's syndrome and Hughes Stovin syndrome: a comparative study

Clin Exp RheumatolPublished Comparative study of a systematic literature review of case reports and a tertiary-centre cohort

Authors' conclusion

Our study indicates that HSS is indeed an 'incomplete form of BS'.

Study context

Population
Hughes-Stovin syndrome (HSS) case reports (2000–2023) and Behçet's syndrome (BS) patients with pulmonary artery involvement at a tertiary centre in Turkey
Participants
58 vs 74
Exposure
HSS cases from the literature vs BS patients with pulmonary artery involvement
  • HSSn = 58
  • BSn = 74reference
Outcome
Demographic and clinical features
Methodological detailshead-to-head comparison, single tertiary centre (Turkey)
  • Head-to-head comparison
  • Single tertiary centre (Turkey)

Main finding

As reported in the abstract

Demographic, clinical and histopathological features
  • BS and HSS comparable for several demographic, clinical and histopathological features
  • Pulmonary artery aneurysms (PAA) significantly more frequent in HSS than in BS
  • Isolated pulmonary artery thrombosis (PAT) less common in HSS than in BS

Observational data: associations, not effects.

Further findings

HSS more likely treated with anti-coagulants and vascular or surgical interventions, less likely to receive immunosuppressive treatment, than BS

Original publication

Pulmonary artery involvement due to Behçet's syndrome and Hughes Stovin syndrome: a comparative study. Clin Exp Rheumatol. Published 5 November 2023. doi:10.55563/clinexprheumatol/t3i6xc

Composed by AI from the published abstract and checked against it. How Briefs are made →

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