Pediatric rheumatology

Highlights from the breakout session: vasculitis in paediatric rheumatology

Rheumatology (Oxford)Published Conference report

Authors' conclusion

The workshop underscored the importance of continued research and tailored therapeutic strategies to improve outcomes in pediatric vasculitis, paving the way for advancements in diagnosis, management, and understanding of these complex diseases.

Study context

Population
Paediatric vasculitis, including IgA Vasculitis (IgAV), Kawasaki Disease (KD) and monogenic vasculitides (e.g. deficiency of ADA2)
Methodological detailsbreakout session highlights, 21st International Vasculitis Workshop, 21st International Vasculitis Workshop, Barcelona, Spain, April 7 to 10, 2024
  • Breakout session highlights
  • 21st International Vasculitis Workshop
  • 21st International Vasculitis Workshop, Barcelona, Spain, April 7 to 10, 2024

Main finding

As reported in the abstract

  • Ankara 2008 criteria for IgAV (endorsed by EULAR and PReS) in adults: high sensitivity, specificity needs further refinement
  • Genetic associations (Human Leukocyte Antigen (HLA) polymorphisms in IgAV) and biomarkers (S100A8/A9, HMGB1, RAGE) presented
  • KD: novel anti-apolipoprotein A-2 antibodies showed promise in reducing coronary arteritis
  • Monogenic vasculitides (e.g. deficiency of ADA2) addressed with new consensus-driven recommendations

Original publication

Highlights from the breakout session: vasculitis in paediatric rheumatology. Rheumatology (Oxford). Published 12 March 2025. doi:10.1093/rheumatology/keae406

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