Autoinflammatory & rare systemic diseases
The 2022 EULAR / ACR Points to Consider at the Early Stages of Diagnosis and Management of Suspected Haemophagocytic Lymphohistiocytosis/Macrophage Activation Syndrome ( Haemophagocytic Lymphohistiocytosis (HLH) / Macrophage Activation Syndrome (MAS) )
Methodological detailsEULAR/ACR, systematic literature review, Delphi methodology, multinational, multidisciplinary task force
- EULAR/ACR
- Systematic literature review
- Delphi methodology
- Multinational, multidisciplinary task force
Recommendations
As issued by the authors
6 overarching statements and 24 specific points to consider
Major themes: prompt syndrome recognition, systematic evaluation of underlying contributors, early intervention targeting both hyperinflammation and likely contributors, careful monitoring for progression/complications and expert multidisciplinary assistance
Original publication
The 2022 EULAR / ACR Points to Consider at the Early Stages of Diagnosis and Management of Suspected Haemophagocytic Lymphohistiocytosis/Macrophage Activation Syndrome ( HLH / MAS ). Arthritis Rheumatol. Published 24 July 2023. doi:10.
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